Aim Laryngeal amyloidosis is a rare condition characterised by localised deposition of amyloid protein in the larynx accounting for 0.2% of benign laryngeal lesions. This study aims to provide insight into the management of this rare condition, highlight important clinical considerations, and explore the outcomes of various treatment modalities. Methodology A mixed case report and literature review was conducted. A 31-year-old male presenting with a 12-month history of worsening dysphonia diagnosed with local amyloidosis and management with local debridement and rheumatology and haematology input and surveillance. The literature review was conducted using medical databases, including PubMed, Medline, and Scopus, to identify relevant studies on laryngeal amyloidosis. Search terms included "laryngeal amyloidosis," "larynx," and "amyloid deposition". Results Laryngeal amyloidosis is a rare` but significant condition that can mimic other benign and malignant pathologies of the larynx, often leading to diagnostic challenges. Laryngeal amyloidosis should be a differential in patients presenting with persistent dysphonia, dyspnoea, and laryngeal mass who are otherwise young and healthy or who have evidence of systemic amyloidosis. Direct visualisation, CT/MRI imaging and biopsy with Congo red staining confirms diagnosis. In the case of local laryngeal amyloidosis treatment strategies, including local surgical excision and observation. However adjunctive haematological therapy should be considered in systemic disease. Recurrence is a known complication, emphasising the need for long-term follow-up. Conclusion Laryngeal amyloidosis, though rare, should be considered in the differential diagnosis of laryngeal masses. This case report, along with the literature review, provides valuable insight into the presentation, diagnosis, and management of laryngeal amyloidosis, highlighting the importance of individualised treatment plans and vigilant post-treatment monitoring to reduce the risk of recurrence.